Journal of Advances in Medical and Biomedical Research Journal of Advances in Medical and Biomedical Research J Adv Med Biomed Res Medical Sciences http://journal.zums.ac.ir 52 journal52 1606-9366 2676-6264 10.30699/jambr en jalali 1401 10 1 gregorian 2023 1 1 31 144 online 1 fulltext
en Pacman Heart as a Congenital Cardiac Defect Associated with Flail Mitral Valve and a Partial form of Shone's Complex; A Case Report Clinical Medicine Clinical Medicine گزارش موردی Case Report Article <p style="text-align: justify;"><span style="font-size:16px;"><span style="font-family:Times New Roman;"><span style="line-height:2;"><span style="unicode-bidi:embed">Partial muscular inter-ventricular septal defect (VSD) or Pacman heart is a rare congenital or occasionally acquired anomaly. Concurrent Pacman heart and Shone&#39;s complex are extremely rare and have never been reported until now. We described a 37-year-old male patient with congenital Pacman heart, flail mitral valve (FMV), and a history of multiple congenital anomalies, including subvalvular aortic stenosis, bicuspid aortic valve (AV), and coarctation of the aorta compatible with the incomplete form of Shone&#39;s complex. Cardiac surgery was not necessary to perform for this anomaly due to the absence of a left-to-right shunt through this partial defect.</span></span></span></span></p> Flail mitral leaflet, Congenital heart defects, Bicuspid aortic valve 100 102 http://journal.zums.ac.ir/browse.php?a_code=A-10-5952-2&slc_lang=en&sid=1 Seyed Hashem Sezavar hsezavar@yahoo.com 5200319475328460074810 5200319475328460074810 No Research Center for Prevention of Cardiovascular Diseases, Institute of Endocrinology & Metabolism, Iran University of Medical Sciences, Tehran, Iran Mahboubeh Pazoki shamimmoghadasi@gmail.com 5200319475328460074811 5200319475328460074811 Yes Dept. of Cardiovascular Diseases, Hazrat-e-Rasool General Hospital, Iran University of Medical Sciences, Tehran, Iran Nehzat Akiash akiash.n@gmail.com 5200319475328460074812 5200319475328460074812 No Atherosclerosis Research Center, Ahvaz Jondishapur University of Medical Sciences, Ahvaz, Iran Farzad Dashti farzad.d@gmail.com 5200319475328460074813 5200319475328460074813 No Research Center for Prevention of Cardiovascular Diseases, Institute of Endocrinology & Metabolism, Iran University of Medical Sciences, Tehran, Iran Pegah Joghataie pegijo57@gmail.com 5200319475328460074814 5200319475328460074814 No Dept. of Cardiovascular Diseases, Hazrat-e-Rasool General Hospital, Iran University of Medical Sciences, Tehran, Iran