Appendiceal mucocele is a rare condition, characterized by the dilation and obstruction of the appendix owing to the accumulation of intraluminal mucus. This study presents a case of appendiceal mucocele and outlines the diagnostic as well as therapeutic approach employed. A 54-year-old female patient presented with abdominal pain, nausea, a bitter taste in her mouth, and constipation which had persisted for 20 days. Upon admission, she underwent laboratory tests and imaging diagnostics. Although initially scheduled for laparoscopic surgery, the procedure was converted to open surgery following the diagnosis of appendiceal mucocele. Torsion of the appendix in three loops was observed intraoperatively. An abdominal assessment revealed no signs of malignancy, with only the distended appendix resected. Postoperatively, the patient experienced no complications and was discharged without pain or infection. Given the potential presence of appendiceal mucocele, for patients presenting with symptoms that mimic acute appendicitis, including abdominal pain, nausea, and vomiting, diagnostic investigations such as computed tomography (CT) and ultrasound are essential.