دوره 26، شماره 114 - ( 1-1397 )                   جلد 26 شماره 114 صفحات 134-127 | برگشت به فهرست نسخه ها

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Babaei M, Ramezanpour A. Papillon-Lefèvre Syndrome in 4 years Old Patient: A Rare Case Report and 3 YearsFollow- Up. J Adv Med Biomed Res 2018; 26 (114) :127-134
URL: http://journal.zums.ac.ir/article-1-4968-fa.html
بابایی مریم، رمضانپور افشار. سندروم پاپیلون لفور در یک کودک 4 ساله: گزارش یک مورد بیماری نادر و پیگیری سه ساله آن. Journal of Advances in Medical and Biomedical Research. 1397; 26 (114) :127-134

URL: http://journal.zums.ac.ir/article-1-4968-fa.html

سندروم پاپیلون لفور در یک کودک 4 ساله: گزارش یک مورد بیماری نادر و پیگیری سه ساله آن
مریم بابایی* 1، افشار رمضانپور2
1- دانشگاه علوم پزشکی زنجان، زنجان ، m.babaei@zums.ac.ir
2- دانشگاه علوم پزشکی زنجان، زنجان
چکیده:   (148624 مشاهده)

Papillon-Lefèvre syndrome is an extremely rare autosomal recessive condition. It is characterized by severe destruction of the periodontium and hyperkeratotic skin lesions on palms, soles, knees, elbows and in some cases calcification of the Dura. The features usually appear together between the ages of 2 and 4 years. Severe periodontal destruction leads to the early shedding of primary and permanent dentition.
Case presentation: A 4-year-old male child was referred to our private clinic with a chief complaint of pain and mobility of the teeth and difficulty in mastication. He had severe mobility in molar teeth. Erythematous keratotic plaques in palms and soles were revealed. According to clinical, radiographic features and pathologic findings, the patient was diagnosed as Papillon-Lefèvre syndrome occurring for the first time in Zanjan. He received periodontal and dermatological treatments.
Conclusion: Papillon-Lefèvre syndrome affects the quality of life at a very young age. Since the patient features are common to periodontics and dermatologists, full awareness of how to diagnose and manage these feature seems crucial for both fields. Early diagnosis of PLS improves prognosis and quality of life in these patients.

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نوع مطالعه: کارآزمایی بالینی |
دریافت: 1396/9/26 | پذیرش: 1396/9/26 | انتشار: 1396/9/26
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