Volume 31, Issue 144 (January & February 2023)                   J Adv Med Biomed Res 2023, 31(144): 100-102 | Back to browse issues page


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Sezavar S H, Pazoki M, Akiash N, Dashti F, Joghataie P. Pacman Heart as a Congenital Cardiac Defect Associated with Flail Mitral Valve and a Partial form of Shone's Complex; A Case Report. J Adv Med Biomed Res 2023; 31 (144) :100-102
URL: http://journal.zums.ac.ir/article-1-6652-en.html
1- Research Center for Prevention of Cardiovascular Diseases, Institute of Endocrinology & Metabolism, Iran University of Medical Sciences, Tehran, Iran
2- Dept. of Cardiovascular Diseases, Hazrat-e-Rasool General Hospital, Iran University of Medical Sciences, Tehran, Iran , shamimmoghadasi@gmail.com
3- Atherosclerosis Research Center, Ahvaz Jondishapur University of Medical Sciences, Ahvaz, Iran
4- Dept. of Cardiovascular Diseases, Hazrat-e-Rasool General Hospital, Iran University of Medical Sciences, Tehran, Iran
Abstract:   (11411 Views)

Partial muscular inter-ventricular septal defect (VSD) or Pacman heart is a rare congenital or occasionally acquired anomaly. Concurrent Pacman heart and Shone's complex are extremely rare and have never been reported until now. We described a 37-year-old male patient with congenital Pacman heart, flail mitral valve (FMV), and a history of multiple congenital anomalies, including subvalvular aortic stenosis, bicuspid aortic valve (AV), and coarctation of the aorta compatible with the incomplete form of Shone's complex. Cardiac surgery was not necessary to perform for this anomaly due to the absence of a left-to-right shunt through this partial defect.

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✅ Partial muscular inter-ventricular septal defect (VSD) or Pacman heart is a rare congenital or occasionally acquired anomaly. Concurrent Pacman heart and Shone's complex are extremely rare and have never been reported until now.


Type of Study: Case Report Article | Subject: Clinical Medicine
Received: 2021/08/6 | Accepted: 2022/06/20 | Published: 2022/12/12

References
1. Shih BC, Lim JH. Incomplete form of Shone complex in an adult congenital heart disease patient. Korean J Thorac Cardiovasc Surg. 2019;52(2):100-4. [DOI:10.5090/kjtcs.2019.52.2.100] [PMID] [PMCID]
2. Celik AI, Ikikardes F, Karaaslan MB. An unusual image: Pacman heart. J Echocardiogr. 2018;35(8):1245-6. [DOI:10.1111/echo.14052] [PMID]
3. Mohan JC, Shukla M, Mohan V, Sethi A. Parachute mitral valve and pacman deformity of the ventricular septum in a middle-aged male. Indian Heart J. 2016;68 Suppl 2(Suppl 2):S126-s30. [DOI:10.1016/j.ihj.2015.09.012] [PMID] [PMCID]
4. Pujol E, Morales M, Roelandt JR, et al. Partial ventricular septal defect (Pacman Heart). Eur J Echocardiogr. 2008;9(2):316-7. [DOI:10.1093/ejechocard/jem068] [PMID]
5. Abdelnabi MH, Almaghraby A, Saleh Y, Elkafrawy F, Ziada K, ElSamad SA. Concomitant partial ventricular septal defect (Pac-man© heart) and left persistent superior vena cava accidentally discovered in young adult. Acta Cardiol. 2020;75(3):261-2. [DOI:10.1080/00015385.2019.1570657] [PMID]

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